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Patient handout

Malignant Hyperthermia Crisis

PRODUCTION

1. Your condition

This handout is for malignant hyperthermia crisis. Your care team identified this based on: unexplained rising etco2 despite increased minute ventilation (mhaus 2023).

Other reasons your team may use this plan: masseter muscle rigidity / generalized rigidity after succinylcholine (mhaus 2023); rapid rise in core temperature (>=1-2c in 5 min, late finding) (mhaus 2023); prior mh event, known ryr1/cacna1s variant, or first-degree relative susceptible (riazi 2018).

2. Your medications

Take these medications exactly as prescribed. Do not stop or change a dose without talking to your provider.

MedicationStarting doseHowWhenWhat it does
discontinue_volatile_anesthetics_immediatelySTOP all sevoflurane/isoflurane/desflurane/halothaneinhaledimmediateRemoving trigger gas halts ongoing calcium release at the ryanodine receptor (MHAUS 2023)
discontinue_succinylcholine_and_avoid_redoseDO NOT redose succinylcholineIVimmediateSuccinylcholine is a depolarizing trigger; switch to non-depolarizing NMB (rocuronium/vecuronium) (MHAUS 2023)
switch_to_tiva_propofol_remifentanilPropofol infusion + opioid (remifentanil or fentanyl)IVcontinuousMaintain anesthesia without halogenated agents (MHAUS 2023)
hyperventilate_100_percent_o2_clean_circuit100% FiO2 at >=10 L/min flush; consider activated charcoal filters on anesthesia circuitinhaledcontinuousWash out residual volatile; supports increased metabolic O2 demand (MHAUS 2023)
call_mhaus_hotline_24_7MHAUS Hotline 1-800-644-9737 (US/Canada)phoneonceLive expert MH guidance during crisis (MHAUS 2023)

Plan: Malignant Hyperthermia Crisis — MHAUS 2023 sequence: STOP triggers, dantrolene 2.5 mg/kg, treat hyperkalemia + acidosis + dysrhythmia + myoglobinuria

4. When to seek emergency care

Call 911 or go to the nearest emergency room right away if you have:

  • Larach Clinical Grading Scale rank "almost certain" or "very likely" — hypercarbia + acidosis + rigidity + temperature >39C + rhabdomyolysis (Larach 2010)(life-threatening)
  • Masseter muscle rigidity after succinylcholine — early MH warning, especially in pediatric (MHAUS 2023)
  • K+ >=6.5 with hyperkalemic ECG changes (peaked T, widened QRS, sine wave) during MH crisis (MHAUS 2023)(life-threatening)
  • Recurrence of MH signs within 24h of initial crisis (occurs up to 25%) (MHAUS 2023)

5. Follow-up

Referral to MH Diagnostic Center (CHCT / IVCT or RYR1/CACNA1S sequencing); MedicAlert bracelet; family counseling; future anesthetic plan (trigger-free TIVA); MHAUS registry case report (MHAUS 2023, Riazi 2018)

6. Sources

Guideline: MHAUS (Malignant Hyperthermia Association of the United States) Recommendations for Diagnosis and Treatment of Malignant Hyperthermia 2023 + Larach Clinical Grading Scale (Anesth Analg 2010) + Riazi RYR1 post-genomics review (Anesthesiology 2018)

  1. pubmed.ncbi.nlm.nih.gov/20081135
  2. pubmed.ncbi.nlm.nih.gov/28902675
  3. pubmed.ncbi.nlm.nih.gov/9523799