Cardiac tamponade — Type A aortic dissection-related (hemopericardium)
Phase E variant of cardio.cardiac-tamponade.core.v1 — narrowed to Type A aortic dissection-related hemopericardium with tamponade. Inherits drainage + bridge regimen from parent via routing BUT critically OVERRIDES the reflexive full pericardiocentesis with LIMITED ≤50 mL bridge drainage ONLY if hypotensive per Hayashi Circ J 2012 + IRAD subgroup analyses + ACC/AHA 2022 PMID 36066317. Specializes for dissection-specific patterns: anti-impulse therapy with esmolol IV (HR <60) BEFORE adding nicardipine (SBP <120) — isolated vasodilator AVOIDED due to reflex tachycardia propagating dissection (ACC/AHA 2022 Class I); EMERGENT cardiothoracic surgery activated SIMULTANEOUSLY with imaging confirmation; CTA chest definitive (or TEE in unstable patient); thrombolytics ABSOLUTE CONTRAINDICATION; severity triggers cover malperfusion syndrome, dissection extension on serial CT, paraplegia from spinal artery compromise, organ-system progression, and pre-operative arrest scenarios. Long-term BB + ARB anti-impulse therapy (target SBP <130 + HR <70), genetic counseling for heritable connective tissue disorders, lifelong CT surveillance. Manifest pointer reuses cardio.cardiac-tamponade.core.v1 manifest. Design-brief pointer reuses parent (dissection-specific differences documented inline). Status INTEGRATED until terminology + RxNav-validated drug codes are reconciled. Authored 2026-05-15 by shard-06-cardio-acute.
Entry points (5)
- symptomSudden tearing chest/interscapular back pain + Beck triad (hypotension + JVD + muffled heart sounds) — Type A dissection with tamponade until proven otherwise (ACC/AHA 2022 PMID 36066317)tearing_chest_back_pain_with_beck_triad
- imagingSTAT TTE: aortic root dissection flap + pericardial effusion + RV diastolic collapse → Type A dissection-related tamponade (Class I; ACC/AHA 2022; ESC 2014)echo_root_dissection_flap_plus_pericardial_effusion
- imagingCTA chest (definitive when stable enough): ascending aorta dissection flap + hemopericardium → emergent cardiothoracic surgery (Hagan IRAD JAMA 2000)cta_chest_type_a_with_pericardial_blood
- symptomBP/pulse differential between extremities + new hemodynamic instability → suspect dissection with branch-vessel malperfusion + possible tamponade overlay (ESC 2014; ACC/AHA 2022)pulse_or_bp_differential_with_hemodynamic_compromise
- symptomSyncope at presentation in suspected aortic dissection — historically associated with tamponade per IRAD (Hagan JAMA 2000 PMID 10685714)syncope_in_dissection_pt_classic_for_tamponade
Required inputs (10)
- agerequireddemographic • used at CONTEXTOlder patients have higher Type A mortality + worse surgical outcomes; bicuspid valve and connective tissue disorders shift age distribution younger (ACC/AHA 2022 PMID 36066317)
- sbprequiredvital • used at RED_FLAGSHypotension is part of Beck triad AND signals tamponade physiology, malperfusion shock, or aortic rupture; goal SBP <120 with anti-impulse therapy once dissection confirmed (ACC/AHA 2022 Class I)
- hrrequiredvital • used at CONTEXTGoal HR <60 with esmolol BEFORE vasodilator added; reflex tachycardia from isolated vasodilator worsens dissection propagation (ACC/AHA 2022; Erbel ESC 2014)
- echorequiredimaging • used at INITIAL_WORKUPBedside TTE/TEE definitive for tamponade physiology + root dissection flap visualization; TEE preferred if hemodynamically unstable for transport (Class I; ACC/AHA 2022)
- cta_chestrequiredimaging • used at INITIAL_WORKUPGold-standard definitive imaging for dissection extent, branch-vessel involvement, pericardial blood quantification — must be obtained when patient stable for transport (Hagan IRAD JAMA 2000 PMID 10685714)
- connective_tissue_or_aortic_historyrequiredhistory • used at CONTEXTMarfan, Loeys-Dietz, Ehlers-Danlos vascular type, bicuspid aortic valve, prior aortic surgery, hypertension history all modify pre-test probability + recurrence risk (ACC/AHA 2022)
- creatininerequiredlab • used at INITIAL_WORKUPBaseline for contrast-related AKI risk + post-op AKI surveillance + dose-adjustment for any sedation/analgesia
- hemoglobinrequiredlab • used at INITIAL_WORKUPBaseline + serial for hemorrhagic loss + transfusion threshold; massive transfusion likely intraoperatively
- inrrequiredlab • used at INITIAL_WORKUPCoagulopathy reversal pre-OR + tracking massive transfusion balance
- d_dimerlab • used at INITIAL_WORKUPHighly sensitive (>97%) for acute aortic dissection if <500 ng/mL within 24h of symptom onset rules out with high NPV (ACC/AHA 2022 ADD-RS supplement)
12-phase flow (9)
- 1FRAMEType A dissection-related tamponade — DO NOT default to full pericardiocentesis; emergent cardiothoracic surgery is definitive; limited bridge drainage (≤50 mL) ONLY if hypotensive (ACC/AHA 2022; Hayashi Circ J 2012)inputs: sbpadvance: dissection-context tamponade physiology suspected
- 2ENTRYRecognize Beck triad + tearing chest/back pain combination; activate aortic emergency pathway + simultaneous OR mobilization (ACC/AHA 2022 Class I)inputs: ageadvance: aortic dissection clinical pattern recognized
- 3CONTEXTDocument connective tissue disease, prior aortic surgery, hypertension history, anticoagulation status; goals-of-care discussion with surgical-eligibility framing (ACC/AHA 2022)inputs: connective_tissue_or_aortic_historyadvance: dissection-context risk factors fully captured
- 4RED_FLAGSTamponade obstructive shock + dissection-extension/malperfusion overlay (cerebral, coronary, mesenteric, renal, spinal, limb); periarrest physiology (ACC/AHA 2022; Trimarchi IRAD)inputs: sbp, hradvance: shock + malperfusion screened → OR mobilization in parallel with imaging
- 5INITIAL_WORKUPSTAT echo (TTE → TEE if unstable), CTA chest if stable for transport, ECG, troponin, BMP, CBC, type & cross 6 units PRBC + 4 FFP, coags, lactate, ABG, baseline creatinine (ACC/AHA 2022 Class I; ESC 2014)inputs: echo, cta_chest, creatinine, hemoglobin, inractions: panel.cardiac, panel.coag, panel.cbcadvance: echo confirms tamponade + dissection flap + CTA confirms Type A extent
- 6DIFFERENTIALConfirm Type A (ascending aorta involvement) vs Type B (descending only — does not cause tamponade); rule out concomitant rupture into pleural space; assess branch-vessel involvement (Hagan IRAD JAMA 2000 PMID 10685714)advance: Type A confirmed + dissection extent mapped
- 7TREATMENTStep 1 anti-impulse therapy with esmolol IV (HR target <60) BEFORE vasodilator (ACC/AHA 2022 Class I); Step 2 emergent cardiothoracic surgery activation; Step 3 LIMITED pericardiocentesis (≤50 mL) ONLY if hypotensive bridge per Hayashi Circ J 2012 + IRAD subgroup data — full drainage precipitates exsanguination (ACC/AHA 2022; Erbel ESC 2014); Step 4 OR for root repair + intraoperative pericardial drainageinputs: sbpadvance: anti-impulse achieved + OR transfer initiated +/- limited bridge drainage performed
- 8DISPOSITIONOR direct transfer for emergent cardiothoracic surgery (root replacement, valve-sparing root, Bentall, hemiarch/total arch per extent); cardiac surgery + anesthesia + perfusion teams mobilized in parallel (ACC/AHA 2022)advance: OR readiness confirmed + transport plan executed
- 9MONITORINGIntraop TEE for root repair adequacy + pericardial decompression; post-op CCU/ICU surveillance for re-bleeding, malperfusion, AKI, neurologic outcome, paraplegia (spinal artery), graft integrity (ACC/AHA 2022)actions: panel.pleuraladvance: post-op stable + no re-bleeding × 48h + neurologic + renal + spinal cord baseline established