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Patient handout

Miller-Fisher Syndrome (GBS variant)

PRODUCTION

1. Your condition

This handout is for miller-fisher syndrome (gbs variant). Your care team identified this based on: classic mfs triad: ophthalmoplegia + ataxia + areflexia (van doorn 2011 pmid 25023340).

Other reasons your team may use this plan: anti-gq1b antibodies positive — ~85% of mfs (highly specific) (wakerley 2016 pmid 25072194); bickerstaff brainstem encephalitis overlap — mfs triad + encephalopathy + brainstem signs; same anti-gq1b+ spectrum (wakerley 2016); pcb variant overlap — bulbar + neck + upper-limb weakness with sparing of legs (wakerley 2016).

2. Your medications

Take these medications exactly as prescribed. Do not stop or change a dose without talking to your provider.

MedicationStarting doseHowWhenWhat it does
ivig0.4 g/kg/d × 5 d (total 2 g/kg)IVdaily × 5 dEAN/PNS 2023 — IVIG preferred for MFS (Cochrane MFS subgroup PMID 25238327); check IgA pre-IVIG
plasmapheresis (PLEX)5 sessions over 7-10 d (q48h)IV5 sessions q48hRaphael Cochrane PMID 22786475 — alternative; less evidence specifically in pure MFS (EAN/PNS 2023)

Plan: MFS — IVIG preferred (per Cochrane subgroup); supportive + overlap-variant monitoring (Hughes Cochrane 2014 PMID 25238327; EAN/PNS 2023)

3. When to call your provider

Contact your care team if any of the following happen:

  • New deficit or worsening >4 wk → MS / CIDP / NMOSD reconsideration (van Doorn 2011)

4. When to seek emergency care

Call 911 or go to the nearest emergency room right away if you have:

  • Bickerstaff brainstem encephalitis — MFS triad + encephalopathy + brainstem signs (hyperreflexia, central facial weakness) + anti-GQ1b+; T2 brainstem hyperintensity on MRI (Wakerley 2016 PMID 25072194)
  • PCB overlap variant — bulbar + neck + upper-limb weakness with sparing of legs; aspiration risk dominant; anti-GQ1b+ (Wakerley 2016 PMID 25072194)
  • MFS-GBS overlap — MFS triad + limb weakness (typical GBS-pattern weakness); ~25% of MFS evolves to include limb involvement (van Doorn 2011 PMID 25023340)

5. Follow-up

Neuro-ophthalmology follow-up for ophthalmoplegia resolution; gait/balance therapy; usually monophasic full recovery in 2-6 mo (van Doorn 2011)

6. Sources

Guideline: 2023 EAN/PNS GBS Guideline + Hughes Cochrane 2014 + Wakerley 2016 anti-GQ1b syndromes spectrum

  1. pubmed.ncbi.nlm.nih.gov/25238327
  2. pubmed.ncbi.nlm.nih.gov/22786475
  3. pubmed.ncbi.nlm.nih.gov/25023340