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Patient handout

Intestinal malrotation with midgut volvulus

PRODUCTION

1. Your condition

This handout is for intestinal malrotation with midgut volvulus. Your care team identified this based on: bilious vomiting (green / yellow-green) in an infant (especially < 1 month of life) — cardinal alarm signal; malrotation with midgut volvulus until proven otherwise (apsa + aap); emergent surgical consult + stat upper gi series (or directly to or if unstable).

Other reasons your team may use this plan: neonate (< 24 h of life) with bilious emesis — life-threatening; differential includes malrotation-volvulus + duodenal atresia + intestinal atresia; emergent ugi + stat surgery; older child with recurrent / intermittent crampy abdominal pain + chronic vomiting / failure to thrive — atypical malrotation; auto-detorsing intermittent volvulus; whirlpool sign on bedside us (clockwise rotation of smv around sma) — sensitivity 80-90 % in skilled hands; specificity > 95 %; first-line bedside screen.

2. Your medications

Take these medications exactly as prescribed. Do not stop or change a dose without talking to your provider.

MedicationStarting doseHowWhenWhat it does
normal saline / lactated Ringer's20 mL/kg IV bolus over 30-60 min, repeat × 1-2 PRN; max ~ 60 mL/kg total before reassessing for fluid overloadIVbolus PRN with reassessmentAAP pediatric resuscitation principles; SSC peds 2020 if Phoenix-2024 sepsis; resuscitation in parallel with imaging / OR mobilization — do NOT delay OR for fluid completion in the unstable bilious-emesis infant
D5 0.45% NaCl maintenance with electrolytesMaintenance rate with deficit replacement after first void documentedIVcontinuousPre-op + post-op maintenance fluid posture
cefazolin25-30 mg/kg IV single dose at inductionIVpre-op single dosePre-op single-dose antimicrobial prophylaxis for clean elective laparoscopic Ladd; no prolonged course (Cantey SCOUT Lancet Infect Dis 2016 PMID 27452782 stewardship principles)
piperacillin-tazobactam80-100 mg/kg IV q6-8h (piperacillin component) × 5-7 d for source-controlled bowel ischemia / perforation; 7-14 d if uncontrolled sourceIVq6-8hBroad Gram-positive + Gram-negative + anaerobe single-agent backbone for intra-abdominal contamination per Solomkin IDSA intra-abdominal 2010 peds-adapted PMID 20583865
metronidazole10 mg/kg IV q8h (max 500 mg/dose); add to cefotaxime if < 28 d (avoid ceftriaxone; AAP Puopolo 2018)IVq8hAnaerobic cover adjunct; combination alternative to single-agent pip-tazo (Solomkin IDSA 2010 peds-adapted)
cefotaxime50 mg/kg IV q8h (q12h if < 7 d of life and < 2 kg); preferred over ceftriaxone if < 28 d due to bilirubin-displacement risk (AAP Puopolo 2018)IVq8hThird-gen cephalosporin for neonatal-band intra-abdominal source; avoid ceftriaxone in < 28 d due to bilirubin displacement (AAP Puopolo 2018 PMID 30455342)
meropenem20 mg/kg IV q8h × 7-14 d for severe / refractory / hospital-acquired or prior resistanceIVq8hCarbapenem-grade broad-spectrum for severe or hospital-acquired or refractory intra-abdominal sepsis (Solomkin IDSA 2010 peds-adapted)
vancomycin15 mg/kg IV q6-8h; AUC target 400-600 mg·h/L (NOT trough alone) per Rybak IDSA 2020 PMID 32191793IVq6-8hMRSA / Gram-positive line-source cover; AUC monitoring per Rybak IDSA 2020
epinephrine0.05-0.3 mcg/kg/min IV (central access); titrate to age-appropriate MAPIVcontinuousSSC peds 2020 — first-line for cold shock (pediatric phenotype)
norepinephrine0.05-0.5 mcg/kg/min IV (central access); titrate to age-appropriate MAPIVcontinuousSSC peds 2020 — first-line for warm shock (pediatric phenotype)
acetaminophen10-15 mg/kg PO/PR/IV q4-6h PRN (max 60 mg/kg/day in infants; lower than older pediatric ceiling)PO/PR/IVq4-6h PRNFirst-line post-op analgesic in infants; avoid opioids when possible
morphine0.025-0.05 mg/kg IV PRN (HALVED infant doses vs older pediatric); 0.05-0.1 mg/kg IV PRN in older children; monitor respiratory depression with capnographyIVPRN with monitoringFor severe post-op pain; infant respiratory depression risk is elevated; HALVED doses + capnography monitoring
ondansetron0.1-0.15 mg/kg IV (max 4 mg single dose); cautious in infantsIVPRNPost-op anti-emetic; FDA pediatric label considerations; minimal QT risk at single doses

Plan: Pediatric malrotation-volvulus pre-op resuscitation + perioperative antibiotics + RSI + analgesia + vasoactives (APSA + AAP + pediatric anesthesia society + Solomkin IDSA intra-abdominal 2010 peds-adapted + SSC peds 2020 + Cantey SCOUT 2016 stewardship)

3. When to call your provider

Contact your care team if any of the following happen:

  • Recurrent bilious emesis post-discharge → return to ED for repeat UGI + management (~ 2-5 % recurrence post-Ladd)
  • Wound issues (drainage, fever, erythema) → urgent pediatric surgery + ED reassessment
  • Failure to gain weight after expected post-op recovery → pediatric GI + surgery reassessment
  • Short bowel adaptation failure with irreversible TPN dependence → intestinal transplant program referral
  • Family caregiver acute distress / PTSD symptoms after traumatic illness → mental-health referral

4. When to seek emergency care

Call 911 or go to the nearest emergency room right away if you have:

  • Bilious vomiting in an infant (especially < 1 month of life) — CARDINAL ALARM signal; midgut volvulus / malrotation until proven otherwise; emergent surgical evaluation + STAT upper GI series (or directly to OR if unstable); DO NOT delay surgical consult for laboratory workup or fluid resuscitation completion or imaging acquisition logistics (APSA + AAP)(life-threatening)
  • Volvulus with signs of ischemia / necrotic bowel (peritonitis + lactate > 2 mmol/L + hematochezia / melena + sepsis features) — life-threatening; emergent ex-lap within < 2 h; open laparotomy preferred (exposure + viability assessment + easier resection); second-look at 24-48 h if borderline viability (APSA + pediatric GI consensus)(life-threatening)
  • Neonate (< 24 h of life) with bilious emesis — life-threatening; differential includes malrotation-volvulus + duodenal atresia + intestinal atresia; emergent UGI + STAT surgery; cefotaxime + metronidazole substitution for ceftriaxone in < 28 d band (avoid bilirubin displacement) (APSA + AAP + Puopolo 2018)(life-threatening)
  • Suspected malrotation-volvulus in hemodynamically unstable patient — DO NOT delay for imaging; emergent ex-lap; resuscitation in parallel with OR mobilization (APSA pediatric surgical consensus)(life-threatening)
  • Failed Ladd procedure OR extensive bowel necrosis at first operation (> 50-75 % small bowel loss; ileocecal valve loss particularly morbid) — short bowel syndrome risk; staged closure + TPN + intestinal rehabilitation; transplant evaluation in select (APSA + pediatric GI / transplant consensus)
  • Older child / adolescent with recurrent / intermittent crampy abdominal pain + chronic vomiting / failure to thrive — atypical malrotation; auto-detorsing intermittent volvulus; elective UGI series + surgical consult; elective laparoscopic Ladd if positive (APSA)
  • Malrotation in heterotaxy syndrome / CDH / omphalocele / gastroschisis / trisomy 21 / duodenal atresia — high prevalence (40-90 % in heterotaxy; virtually universal in CDH / omphalocele / gastroschisis); intra-operative evaluation + Ladd at time of corrective procedure or staged; prophylactic Ladd in asymptomatic heterotaxy controversial (APSA heterotaxy consensus)
  • Recurrent volvulus post Ladd (~ 2-5 % recurrence rate) — uncommon if Ladd performed correctly; surgical re-evaluation; repeat UGI series + emergent ex-lap if confirmed (APSA pediatric surgical consensus)
  • Short bowel syndrome after extensive resection (> 50-75 % small bowel loss; ileocecal valve loss particularly morbid) — long-term TPN + intestinal rehabilitation + transplant evaluation in select; teduglutide for adaptive failure (APSA + pediatric GI / transplant consensus)

5. Follow-up

Post-op pediatric surgical follow-up at 2-4 weeks for wound check + scar inspection + weight-gain review; pediatrician follow-up within 1-2 weeks for routine well-baby / well-child care including weight-gain trajectory + feeding tolerance; pediatric GI consult at 4-6 weeks for short bowel syndrome management if applicable (TPN tolerance, enteral advance, line-source surveillance, glucagon-like peptide-2 analog teduglutide consideration in select); intestinal transplant program referral for irreversible TPN dependence + life-threatening complications (APSA + pediatric GI / transplant consensus); recurrence surveillance for the ~ 2-5 % post-Ladd recurrence rate (return precautions taught + low threshold for repeat UGI on recurrent symptoms). Heterotaxy / CDH / omphalocele / gastroschisis patients — ongoing multidisciplinary follow-up for index syndrome.

6. Sources

Guideline: APSA (American Pediatric Surgical Association) pediatric surgical-emergency guidance for malrotation + midgut volvulus + AAP infant-vomiting guidance + ACR Appropriateness Criteria — Vomiting in Infants Up to 3 Months of Age + SPR / ACR consensus on UGI series technique (ligament of Treitz position + duodenal C-loop + corkscrew + beak deformity findings; sensitivity ~ 96 %, specificity ~ 98 %) + APSA heterotaxy / CDH / omphalocele / gastroschisis consensus (high malrotation prevalence; prophylactic Ladd controversial) + APSA short bowel syndrome consensus + pediatric GI / transplant programs (long-term TPN + intestinal rehabilitation; teduglutide for adaptive failure; intestinal transplant for irreversible TPN dependence) + Pediatric anesthesia society consensus (RSI for full stomach + aspiration risk; NG decompression pre-op; avoid nitrous oxide in suspected obstruction) + Solomkin IDSA Complicated Intra-Abdominal Infection 2010 PMID 20583865 (peds-adapted for confirmed bowel ischemia + perforation / peritonitis) + SSC peds 2020 (for shock physiology if bowel necrosis precipitates sepsis)

  1. pubmed.ncbi.nlm.nih.gov/20583865
  2. pubmed.ncbi.nlm.nih.gov/32191793
  3. pubmed.ncbi.nlm.nih.gov/27452782