Abdominal aortic aneurysm (surveillance + rupture)
5-step regimen (surveillance + medical optimization → elective repair → post-repair surveillance → ruptured pathway → mycotic) authored with RxCUIs from vasc.aaa.v1 manifest rxnorm_codes block; outpatient + ED + transition setting playbooks; six severity triggers including rupture, rapid expansion, mycotic, CTD, endoleak, suspected unstable. No `_design-brief.md` in src/lib/tier3/problem-package/packages/abdominal-aortic-aneurysm — author one before promoting to PRODUCTION. Manifest cites ESVS 2024, NICE NG156, SVS 2018, ACC/AHA 2022, ESC 2024, RCEM 2019, NHS screening — without inline PMIDs; backfill on next research pass. No AAA-specific calculator (Glasgow Aneurysm Score, Hardman index, ESVS perioperative risk) yet in clinical-tools-registry.ts — flag before PRODUCTION.
Entry points (4)
- symptomPulsatile abdominal mass on exam (SVS 2024)pulsatile_abd_mass
- symptomAbdominal/back pain + hypotension/syncope — rupture suspicion (ESVS 2019; SVS 2024)abd_back_pain_with_hypotension
- imagingUS/CT showing infrarenal aorta >=3.0 cm (SVS 2024; ESVS 2019)us_or_ct_aaa
- problem_listNHS / USPSTF AAA screening — men 65-75 / select women (USPSTF 2019; ESVS 2019)screening_eligible
Required inputs (12)
- agerequireddemographic • used at CONTEXTScreening criteria + repair threshold + life expectancy (SVS 2024; ESVS 2019)
- sexrequireddemographic • used at CONTEXTRepair threshold lower in women ~5.0 cm vs 5.5 cm (SVS 2024; ESC 2024)
- sbprequiredvital • used at RED_FLAGSPermissive hypotension SBP 70-90 mmHg in suspected rupture (ESVS 2019)
- hrrequiredvital • used at RED_FLAGSHemodynamic monitoring + tachycardia screen (SVS 2024)
- cta_aortarequiredimaging • used at INITIAL_WORKUPDefinitive sizing + rupture/contained leak detection (SVS 2024; ESC 2024)
- aortic_usimaging • used at INITIAL_WORKUPScreening + surveillance imaging (ESVS 2019; USPSTF 2019)
- creatininerequiredlab • used at CONTEXTContrast planning; renal artery involvement (SVS 2024)
- crplab • used at BRANCHING_WORKUPInflammatory / mycotic phenotype (ESVS 2019)
- blood_culturelab • used at BRANCHING_WORKUPMycotic AAA workup (ESVS 2019)
- smokinghistory • used at CONTEXTStrongest modifiable risk factor + smoking cessation (SVS 2024; ESVS 2019)
- family_history_aaahistory • used at CONTEXTFirst-degree relative -> earlier screening (SVS 2024; ESVS 2019)
- connective_tissue_disorderhistory • used at CONTEXTMarfan / EDS-vascular / Loeys-Dietz lower threshold (ESC 2024)
12-phase flow (12)
- 1FRAMEDifferentiate stable surveillance vs symptomatic / ruptured emergency (SVS 2024; ESVS 2019)inputs: sbpadvance: phenotype assigned
- 2ENTRYCapture trigger — screening / incidental / symptomatic (SVS 2024; USPSTF 2019)inputs: age, sexadvance: entry trigger captured
- 3CONTEXTSmoking, family history, connective-tissue disorder, comorbidity / fitness for repair (SVS 2024; ESC 2024)inputs: smoking, family_history_aaa, connective_tissue_disorder, creatinineadvance: context complete
- 4RED_FLAGSRupture suspicion -> permissive hypotension SBP 70-90 + STAT vascular + MTP; hemorrhagic shock (ESVS 2019)inputs: sbp, hractions: acute_abdomenadvance: rupture pathway activated or excluded
- 5INITIAL_WORKUPAortic US (screening ESVS 2019); CTA for sizing / morphology / EVAR anatomy (SVS 2024); BMP, CBC, coag, type-and-screeninputs: cta_aorta, creatinineactions: panel.renal, panel.coag, panel.cbcadvance: sizing + morphology documented
- 6BRANCHING_WORKUPMycotic / inflammatory phenotype workup — BC, CRP, ESR, FDG-PET (ESVS 2019); thoracoabdominal extension; iliac involvementinputs: crp, blood_cultureadvance: phenotype subtype documented
- 7DIFFERENTIALInfrarenal vs juxtarenal vs thoracoabdominal; saccular vs fusiform; mycotic vs inflammatory vs degenerative (SVS 2024; ESC 2024)advance: classification documented
- 8RISK_STRATIFICATIONRepair threshold >=5.5 cm men / >=5.0 cm women / rapid expansion >1 cm/y / saccular / symptomatic (SVS 2024; ESC 2024); surveillance interval otherwise (ESVS 2019)inputs: age, sexadvance: repair vs surveillance decision documented
- 9TREATMENTRuptured / symptomatic -> EVAR-first (ESVS 2019 Class I; EVAR-1 Greenhalgh Lancet 2004) with permissive hypotension and MTP; elective EVAR vs open repair per anatomy + fitness (SVS 2024); medical optimization — smoking cessation, statin, BP control; mycotic -> long-course IV abx + early repair (ESVS 2019)inputs: sbpadvance: repair plan and medical optimization documented
- 10DISPOSITIONSymptomatic / ruptured -> vascular OR; elective surveillance -> vascular surgery clinic (SVS 2024); med optimization in primary careadvance: disposition assigned
- 11MONITORINGSurveillance interval by size (ESVS 2019; SVS 2024); post-EVAR endoleak surveillance — CT/duplex 1, 6, 12 mo then annual (SVS 2024); post-open follow-upadvance: surveillance plan documented
- 12FOLLOWUPLong-term smoking cessation; BP and statin optimization; family screening recommendations (SVS 2024; ESC 2024)advance: long-term plan in place